what is haemophilia

Hemophilia comes from the Ancient Greek language, which consists of two words namely Haima meaning blood and philia meaning love or affection.
Hemophilia is an inherited disease, which means inherited from the mother to her child while the child is born.

Blood in a patient with hemophilia can not be frozen by themselves normally. The process of blood clotting in a patient with hemophilia is not as fast and as much as any other normal person. He will require more time for blood clotting process.

Patients with bleeding disorder hemophilia mostly under the skin, such as if a little bruising clash, or a bruise incurred by itself if the patient has been doing heavy activity; swelling in the joints, such as knee, ankle or elbow. The suffering of people with hemophilia can be life-threatening if the bleeding occurs in the vital organs such as bleeding in the brain.

Hemophilia A and BHemophilia is divided into two types, namely:- Haemophilia A; which is also known as:

  - Classical Hemophilia; because this type of hemophilia is the most common deficiencies in blood clotting factors.

- Hemophilia Factor VIII deficiency; occur because of lack of factor 8 (Factor VIII) protein in blood that cause problems in the process of blood clotting.

 - Hemophilia B, also known by the name:

  - Christmas Disease; as found for the first time on a man named Steven Christmas from Canada

- Hemophilia Factor IX deficiency; occur because of lack of factor 9 (Factor IX) protein in blood that cause problems in the process of blood clotting.

How is blood clotting disorder that can happen?

Disorders that may occur due to the amount of certain types of blood clotting is less than the normal amount, even almost non-existent. Differences of blood clotting processes that occur between normal individuals (Figure 1) to the hemophiliac (Figure 2).Figure 1 and Figure 2 shows an injured blood vessel in the blood clotting factors contained a substance that plays a role in menghentukan bleeding.

a. When it was bleeding means there is injury to the blood vessels (ie a channel where blood flows throughout the body), then the blood out of the vessel.b. Blood vessels to shrink / shrunk.c. Blood platelets (thrombocytes) will close the wound on the vessel.d. Clotting factors of blood work to make woven (yarns - threads of fibrin), which will close the wound so the blood stopped flowing out of vessels.

      

b.   How many people with hemophilia discovered?

Hemophilia A or B is a disease that is rarely found. Hemophilia A occurs at least - not less than 1 in 10,000 people. Hemophilia B is more rarely found, which is 1 in 50,000 people.

Anyone who may have hemophilia?

Hemophilia knows no race, differences in skin color or ethnicity.
Hemophilia most in suffering only in men. Women will actually have hemophilia if his father was a hemophilia and her mother is pemabawa properties (carrier). And this is very rare. (See decreased Haemophilia)

As the disease were revealed, people will be affected by hemophilia since she was born, but in fact hemophilia always detected in the first year of his birth.

Levels of HemophiliaPatients with severe hemophilia / weight which only had higher levels of factor VIII or factor IX less than 1% of the normal amount in the blood, may experience some bleeding times in a month. Sometimes - sometimes bleeding just happens for no apparent reason.

People with hemophilia are more rare than severe hemophilia bleed. Bleeding often occurs due to the activity of the body that is too heavy, such as excessive exercise.People with mild hemophilia bleed less frequently. They have bleeding problems only in certain situations, such as surgery, tooth extraction or mangalami serious injury. Women pengalami mild hemophilia may be more bleeding during menstruation.

Source: http://www.hemofilia.or.id/hemofilia.php